61. Health Ency.: Disease: Prune Belly Syndrome Ency. home Disease P prune belly syndrome. prune belly syndrome. Causesand Risks. The underlying causes of prune belly syndrome are unknown. http://www.accessatlanta.com/shared/health/adam/ency/article/001269.html

SEARCH: The Web Yellow Pages HOME AJC.COM Illustrated Health Encyclopedia Important notice Ency. home Disease P Prune belly syndrome Overview Symptoms Treatment Prevention Alternative names: Eagle-Barrett syndrome Definition: A disease characterized by three major findings (triad): deficient abdominal muscles (causing the skin of the abdomen to wrinkle like a prune), undescended testicles , and a dilated abnormal urinary tract. Causes and Risks The underlying causes of prune belly syndrome are unknown. There is blockage to the flow of urine from the kidney to the outside of the body during fetal life. For example, dilatation of the urinary tract may develop as a result of urethral obstruction in the womb. The incidence is approximately 1 in 30,000 to 40,000 births. Boys are almost solely affected. Expectant mothers carrying affected infants may develop varying degrees of oligohydramnios (insufficient amniotic fluid ) that predisposes the infant to lung problems (see Potter syndrome ). The newborn infant has a wrinkled abdomen (it looks like a prune). This appearance results from swelling with fluid in the womb then loss of that fluid after birth leading to wrinkles of excess skin. The appearance is accentuated by the lack of adequate abdominal musculature. Genital abnormalities may be prominent as undescended testes . Approximately one third of the infants are either stillborn or die within the first few weeks of life from severe lung, kidney, or combined problems.

62. The Indian Journal Of Radiology And Imaging - Images Key words Congenital anomalies, Genitourinary system, Ultrasound, prunebelly syndrome. prune belly syndrome Clinical paediatric uroradiology. http://www.ijri.org/archives/20011101/images01.htm

Images: Prune Belly Sydrome: Antenatal Ultrasound GANESHAN S, INDRAJIT IK, Ind J Radiol Imag 2001; 11:1: 25-28 Key words: Congenital anomalies, Genitourinary system, Ultrasound, prune belly syndrome The Prune Belly syndrome (abdominal muscles deficiency syndrome, Eagle Barret syndrome) in its complete form is characterized by deficiency of abdominal wall muscles, undescended testis and dilated urinary tract. This syndrome has derived its name from the wrinkled prune like appearance of the abdominal wall [ ]. Sonographic observations in three cases of Prune Belly syndrome, prenatally diagnosed and subsequently confirmed are presented in a pictorial essay. Pathology Prune Belly syndrome (PBS), an uncommon condition, results from failure of the lateral mesoderm to migrate or differentiate into the musculature of the abdominal wall and urinary tract which normally occurs by about the tenth week of fetal life [ ]. Even though associated ureteral anomalies like megaloureter, bulbar or penile urethral diverticulum may occur, classically no evidence of any intrinsic urethral obstruction can be demonstrated [

63. Prune Belly Phenotype.... dysplasia. Key words prune belly syndrome, lower urinary tract anomalies,urethral obstruction sequence, renal dysplasia. Key Ur 741. http://www.imbiomed.com.mx/Urologia/Urv57n4/english/Zur74-1.html

García-Escandón IN, De la Fuente-Cortez BE, Rodríguez-Bonito R, Guajardo-González CD. Rev Mex Urol ABSTRACT Prune belly, a phenotype syndrome consists of a muscular deficiency of the abdominal wall causing a prune like appearance, urinary tract alterations and bilateral cryptorquidism. In female it produces a bihorn uterus and vaginal athresia. Its prevalence is 3.4 100,000 live births. The male:female ratio is 5:1. There are two theories that account for its pathogenesis: one of them proposes that there is a mesenchymal dysplasia and the other explains it as the outcome of an urethral obstruction. It could be ranked as a syndrome or sequence according to Smith and since they are used indistinctly in the literature, we explain the difference on the basis of a patient that shows prune belly phenotype with urethral obstruction sequence and athresia due to a mesenchymal defect that damages other organs and is expressed as incomplete intestinal rotation, upper anorectal malformation, renal hypoplasia dysplasia and uracus channel persistence all of which is associated to a mesenchymal dysplasia.

64. Prune Belly Syndrome prune belly syndrome,, Print this article, prune belly syndrome, Fig.1 Intravenous urography of a child with prune belly syndrome. http://www.amershamhealth.com/medcyclopaedia/Volume VII/prune belly syndrome.htm

Medcyclopaedia About Medcyclopaedia Amersham Health Search for: Type a word or a phrase. All forms of the word are searchable. Advanced search Browse entry words starting with: A B C D ... Other characters Try our Medcyclopaedia Premium Edition with added tools and functionality tailored to make your working day easier. The following tools are presently available: Expanded search *For Medical Professionals only, registration required Prune belly syndrome, a triad of features consisting of deficient abdominal wall muscles, urinary tract dilatation and cryptorchidsim. The most recognizable feature of this condition is irregularity of the skin of the abdominal wall with underlying abdominal wall muscle atrophy. The urinary tract manifestations include dilatation of the bladder, hydroureter, hydronephrosis and bladder neck dilatation. The kidneys may be small and dysplastic but stretched around the dilated collecting systems ( Fig.1 The condition may be suspected in utero although the diagnosis is rarely made until post natal life. The bladder may have a prominent superior margin due to a urachal remnant. The ureter is often dysplastic and has a prostatic utricle ( Fig.2

65. Prune Belly Syndrome prune belly syndrome,, Print this article, The incidence is 1 in 35,000–50,000live births. prune belly syndrome occurs almost exclusively in males. http://www.amershamhealth.com/medcyclopaedia/Volume IV 2/prune belly syndrome.ht

Medcyclopaedia About Medcyclopaedia Amersham Health Search for: Type a word or a phrase. All forms of the word are searchable. Advanced search Browse entry words starting with: A B C D ... Other characters Try our Medcyclopaedia Premium Edition with added tools and functionality tailored to make your working day easier. The following tools are presently available: Expanded search *For Medical Professionals only, registration required Prune belly syndrome, a congenital absence or hypoplasia of the anterior abdominal wall musculature, accompanied by a generalized dilatation of the urinary tract and bilateral cryptorchidism. The condition is also known as Eagle – Barrett or triad syndrome. The incidence is 1 in 35,000–50,000 live births. Prune belly syndrome occurs almost exclusively in males. The condition occurs sporadically, and the aetiology is unknown. A genetic predisposition has been proposed, and the occurrence of prune belly syndrome in siblings has been reported. Curiously, the condition is commoner in twin pregnancies. All reported twins have been discordant for the syndrome. renal failure Antenatal ultrasound (US) may suggest the diagnosis of prune belly syndrome, when hydroureteronephrosis with a large bladder and flaccid-appearing abdominal wall are detected. However, the prenatal distinction from severe vesicoureteric reflux or posterior urethral valves may be difficult. Postnatally, hydroureteronephrosis and bladder enlargement may be demonstrated by US, CT, MRI, or intravenous urography.

66. Prune Belly Syndrome From Medicine, Ob/Gyn, Psychiatry, And Surgery / Urology prune belly syndrome In 1839, Frölich first described PBS, and Osler gavethe condition its name. Stephens FD Four valves in prune belly syndrome. http://author.emedicine.com/med/topic3055.htm

eMedicine Journal Medicine, Ob/Gyn, Psychiatry, and Surgery Urology Prune Belly Syndrome Synonyms, Key Words, and Related Terms: PBS, Eagle-Barrett syndrome, triad syndrome Author Information Introduction Indications Relevant Anatomy And Contraindications ... Bibliography AUTHOR INFORMATION Section 1 of 12 Authored by Israel Franco, MD , Assistant Professor, Departments of Urology and Pediatrics, Division of Pediatric Urology, New York Medical College Israel Franco, MD, is a member of the following medical societies: American Academy of Pediatrics American College of Surgeons American Urological Association Endourological Society ... Medical Society of the State of New York , and Society of Laparoendoscopic Surgeons Edited by Peter Langenstroer, MD , Assistant Professor, Department of Surgery, Division of Urology, Medical College of Wisconsin; Francisco Talavera, PharmD, PhD , Senior Pharmacy Editor, eMedicine; Shlomo Raz, MD , Professor, Department of Surgery, Division of Urology, University of California at Los Angeles School of Medicine; J Stuart Wolf, Jr, MD

67. Health Library Find Information On Prune Belly Syndrome At Find information on prune belly syndrome at MerckSource. Learn moreabout prune belly syndrome. Definition A disease characterized http://www.mercksource.com/pp/us/cns/cns_hl_adam.jspzQzpgzEzzSzppdocszSzuszSzcns

68. Belly Gut Stomach Belch Medical Etymology Arts Human Overview famous American medical pioneer. Osler described the prune belly syndromewhich is a very serious BIRTH DEFECT. Osler noted that http://www.consultsos.com/pandora/in240602.htm

Classic Etymology Medicine - Mythology - Arts - Sciences Medical Etymology MedWord WordWise Genealogy Nature and Sense in Words Notes, Comments and Reflections Pandora's Word Box W. Wertelecki, M.D. Comments Requests Links to Key Word Ideas Abducent Abdomen Abdominal Exstrophy Abdominal Wall Defect ... Wiedemann Beckwith S. BELLY GUT STOMACH BELCH Following an overview of ESOPHAGUS STOMACH GASTRIC ABDOMEN and VENTRAL we focus now on the more vernacular terms BELLY and GUT. Prominent "gut". According to some authorities, BELLY arose from "bely" and is one of the most ancient "English" words. Currently this word is considered to be somewhat coarse. In any case, BELLY conveys ideas also found in BELOW and BELLOW as well as in BAG, BULGE and BUDGET. Ideas in words rarely are limited to one language. From other tongues, it is obvious that BELLY has to do with BELCH, BARK, and VOICE. An example is provided by laryngeal cancer victims who lose their vocal cords. By mastering ERUCTATION and BELCHING gastric gas through their oral cavity, such patients are able to regain some ability to verbalize. Often obesity has an early start.

69. THIS IS A STUDENT REPORT AND MAY CONTAIN INACCURACIES I. prune belly syndrome, also known as EagleBarrett Syndrome, by Jill Todd.II. prune belly syndrome – Levitt . Pediatric Urology Associates, PC. http://a-s.clayton.edu/hampikian/1901H/REPORTS1999/PruneBelly1901h-01.htm

THIS IS A STUDENT REPORT AND MAY CONTAIN INACCURACIES. IF YOU WISH TO QUOTE FROM IT YOU MUST GET THE WRITTEN PERMISSION OF DR. GREG HAMPIKIAN greghampikian@mail.clayton.edu I. Prune Belly Syndrome, also known as Eagle-Barrett Syndrome, by Jill Todd II. Chromosomal Location Prune Belly mimics an X-linked disease. The exact cause of Prune Belly Syndrome is not known; although, urinary obstruction (a common symptom), has been associated with the Ring X chromosome which lacks the XIST locus. The XIST is the inactivation center. Failure for the Ring X chromosome to become inactive causes many abnormalities, such as urinary obstruction (Wiley, 1). III. Type of inheritance Prune Belly Syndrome is an autosomal dominant disease; however, it mimics X-linked inheritance. This disease is seen in families – only in sons. The disease is thought to be caused by a primary defect in mesoderm development (Dept of Radiology, 1). Incidence Approximately 1/40,000 live births are born with Prune Belly Syndrome. 20% are still born or die before birth; 50% die in the first two years of life (D’Alessandro, 1). The disease is predominately in males. Symptoms Absence or partial stomach muscles Abdomen appears as a "potbelly" (Pedbase, 2)

70. WebGuest - Open Directory : Health : Conditions And Diseases : Genetic Disorders Top Health Conditions and Diseases Genetic Disorders prune belly syndrome(3). See also Health Conditions and Diseases Rare Disorders (128). Sites http://directory.webguest.com/index.cgi/Health/Conditions_and_Diseases/Genetic_D

Browse thru 1000's of books about health, mind and body: About Us Privacy Statement Acceptable Use Policy Legal Notices ... Contact Us the entire directory only in Top Health Conditions and Diseases Genetic Disorders : Prune Belly Syndrome See also: Health: Conditions and Diseases: Rare Disorders Sites: NORD - Prune Belly Syndrome - Offers a list of synonyms, a general discussion and further resources. Pediatric Database - Offers a definition of Prune Belly Syndrome, the epidemiology, pathogenesis, pathology, clinical features, investigations and management. Prune Belly Syndrome Network - Devoted to health education, information and support for the person with the condition as well as their friends, families or the health professionals who treat them. Also known as Eagle-Barrett syndrome. Last update: 4:32 PT, Friday, May 18, 2001 Help build the largest human-edited directory on the web. Submit a Site Open Directory Project Become an Editor

71. Directory :: Look.com prune belly syndrome (3) See Also. Sites. NORD prune belly syndrome Offersa list of synonyms, a general discussion and further resources. http://www.look.com/searchroute/directorysearch.asp?p=551856

72. Department Of Urology Mount Sinai School Of Medicine prune belly syndrome What is prune belly syndrome? prune belly syndromeis an extremely unusual condition. This occurs in males http://www.mssm.edu/urology/pediatric_urologic_problems.shtml

Pediatric Urologic Problems ediatric urology provides management of problems of the urinary tract and genitalia in children and adolescents. This field encompasses many diseases from the very common such as hydroceles (collection of fluid around the testicles) and hernias to the very rare such as ambiguous genitalia and exstrophy (an abnormality of formation of the bladder and bony pelvis). An understanding of embryology, anatomy and physiology are crucial to dealing with these congenital disorders. Pediatric Kidney Diseases Hydronephrosis Tumors of the Kidney Kidney Stones ... Contact Information Pediatric Kidney Diseases As maternal obstetrical sonographies have become more prevalent, obstetricians, neonatologists and pediatric urologists have become exposed to a wide variety of abnormalities detected during pregnancy. Over half of the prenatally detected abnormalities are related to the genitourinary system. By far the most common prenatally detected abnormality is hydronephrosis. Hydronephrosis What is Hydronephrosis?

73. Developmental Back to Top. Fig. 6 prune belly syndrome Occurs predominantly in malesas a result of bladder outlet obstruction from multiple etiologies. http://www.medsch.wisc.edu/path703/slide/lectslides/develop.html

Developmental Figures: Back to Lecture Slide Menu Fig. 1 Potter Sequence: Potter sequence results from oligohydramnios (decreased amniotic fluid). The phenotype of flattened facies, wide nasal bridge, positional abnormalities of the hands and feet, and hypoplastic lungs result from fetal compression and decreased fetal movement due to the lack of amniotic fluid. The major cause of death in the newborn is pulmonary hypoplasia. Back to Top Fig. 2 Normal Placenta: Pathologists can determine the type of twinning from examination of the intervening membranes between gestational sacs. A placental membrane of a normal singleton pregnancy consists of the amnion (cuboidal epithelium and thin layer of subjacent connective tissue), the chorion (layer of connective tissue and cells), and the trophoblasts (fetal in origin) that merge with the decidua (maternal in origin). Back to Top Fig. 3 Diamniotic dichorionic twin: Dizygotic twins and monozygotic twins that split very early in development have diamniotic, dichorionic membranes separating them. There are two amnions, two chorions, and an intervening trophoblastic layer. Back to Top Fig. 4

74. Wellspent.org - Shop, Save And Support! prune belly syndrome Network. Fundraising Needs In order to continueour annual conventions, we are in need of some funds to help http://www.wellspent.org/Causes/CauseInfo?c=819

75. Abnormalities, Multiple prune belly syndrome Search PUBMED for prune belly syndrome AllReview Therapy Diagnosis; prune belly syndrome Columbia U. Prune http://www.ohsu.edu/cliniweb/C16/C16.131.77.html

Abnormalities, Multiple Back to previous level Alagille Syndrome Search PUBMED for Alagille Syndrome: All Review Therapy Diagnosis ... Arteriohepatic Dysplasia or Alagille Syndrome: Vanderbilt U. Angelman Syndrome Search PUBMED for Angelman Syndrome: All Review Therapy Diagnosis ... Angelman Syndrome: U. of Reading Basal Cell Nevus Syndrome Search PUBMED for Basal Cell Nevus Syndrome: All Review Therapy Diagnosis ... Basal Cell Nevus Syndrome: Med. Coll. of Wisconsin Beckwith-Wiedemann Syndrome Search PUBMED for Beckwith-Wiedemann Syndrome: All Review Therapy Diagnosis ... Beckwith-Wiedemann Syndrome: Med. Coll. of Wisconsin Bloom Syndrome Search PUBMED for Bloom Syndrome: All Review Therapy Diagnosis Branchio-Oto-Renal Syndrome Search PUBMED for Branchio-Oto-Renal Syndrome: All Review Therapy Diagnosis Cockayne Syndrome Search PUBMED for Cockayne Syndrome: All Review Therapy Diagnosis ... Cockayne syndrome: Med. Coll. of Wisconsin Cri-du-Chat Syndrome Search PUBMED for Cri-du-Chat Syndrome: All Review Therapy Diagnosis ... Cri-du-Chat Syndrome: OMIM De Lange's Syndrome Search PUBMED for De Lange's Syndrome: All Review Therapy Diagnosis Down Syndrome Search PUBMED for Down Syndrome: All Review Therapy Diagnosis ... Down syndrome, facial features, gross: U. of Utah Webpath

76. Mioti: Medical Condition Condition prune belly syndrome. DermAtlas prune belly syndrome.The dermatlas Web. MEDLINEplus prune belly syndrome. MEDLINEplus http://www.mioti.com/cat/condition/condition.asp?Cat=PruneBelly

77. Untitled Translate this page Key Words prune belly syndrome, Hipoplasya Abdominal Wall, Bilateral Crysptorchidia,Dilatation Urinary Tract. *Dr. Alexander P. Gómez, **Dra. http://www.infomedonline.com.ve/medifami/art72art4.htm

Revista Venezolana y Regional Andina de Atención Médica Primaria SÍNDROME DE PRUNE BELLY REPORTE DE UN CASO *Dr. Alexander P. Gómez, **Dra. Dinorah L. Rivas Durán, **Dr. Jesús A. Rivas Durán, ***José A. Mesa RESUMEN: Revisando la literatura nacional encontramos escasa información referente al Síndrome de Prune Belly o Síndrome de Abdomen en Ciruela Pasa, lo que motivó nuestro interés en la revisión del tema a propósito de la presentación del primer caso hospitalizado en el Hospital “Dr. Plácido D. Rodríguez R.”. Este síndrome se caracteriza por la ausencia o hipoplasia congénita de la pared abdominal, severa dilatación no obstructiva del tracto urinario y criptorquídia bilateral (1). Siendo una patología de etiología aún obscura y de difícil manejo, es importante su estudio dado la gravedad de los trastornos fisiopatológicos que ocasiona este complejo malformativo. Se presenta el caso de neonato masculino quien nació con dificultad respiratoria, hipoplasia de la pared abdominal, criptorquidia bilateral y dilatación del tracto urinario. Se realizaron estudios ultrasonográficos y radiológicos que confirmaron el diagnóstico. La anomalía no urológica más importante fue dextrocardia. Palabras Claves: Síndrome de Prune Belly, Hipoplasia Pared Abdominal, Criptorquídia Bilateral, Dilatación Tracto Urinario.

78. The Lethal Variant Of The Prune Belly’s Syndrome. Two Cases Report produced lethal development malformations. Key words prune belly syndrome,urethral obstruction, renal dysplasia, lethal variant. http://www.medigraphic.com/ingles/i-htms/i-h-gral/i-hg1999/i-hg99-3/ir-hg993j.ht

Durán PM, Rivero de JV, Macías JB The lethal variant of the Prune Belly’s syndrome. Two cases report Original title: La variante letal del síndrome Prune Belly. Informe de dos casos Rev Med Hosp Gen Mex 1999; 62 (3): 206-209 ABSTRACT Two cases of the lethal variant of syndrome Prune Belly are described in which urethral obstruction produced serious alterations with vesical and ureteral distension with secondary repercussion on the abdominal wall and renal bilateral dysplasia. The theories of the etiopathogeny of this syndrome are commented, those of the mesoderm development alteration of the early obstruction of the urethral that caused abdominal wall malformation. In the two cases, the severity of urinary tract obstruction produced lethal development malformations. Key words: Prune Belly syndrome, urethral obstruction, renal dysplasia, lethal variant.

79. Abdominal Wall Defects (RAHC) omphalocele. The embryology of prune belly syndrome is unknown. InitialManagement. The Problems Heat loss from exposed abdominal contents. http://www.usyd.edu.au/su/anaes/lectures/Abdo_Wall_Defects.html

ABDOMINAL WALL DEFECTS JOHN LOADSMAN 12/10/94 (RAHC) Types of Abdominal Wall Defects Omphalocele/Exomphalos: Congenital herniation of abdominal contents at the umbilicus (i.e. into the umbilical cord). Occasionally divided into: always present but it may have ruptured at or before birth exposing the contents. Gastroschisis: Full thickness abdominal wall defect situated almost always to the right of the umbilicus without a covering membrane. A bridge of skin separates it from the umbilicus. Prune Belly Syndrome: Congenital deficiency of abdominal musculature, urinary tract dilatation and cryptorchidism. There are three grades: I. Severe renal and pulmonary disease incompatible with life. II. Severe uropathy requiring extensive reconstruction. III. Healthy neonates requiring little or no surgery. Others: e.g. Bladder extrophy. Incidence Omphalocele: 1:6,000 Gastroschisis: 1:20,000 - 30,000 Prune Belly: 1:50,000 Associations Omphalocele: 30% have associated congenital defects (? up to 50%). 20% have congenital heart disease, most commonly tetralogy.

80. Clinical Pictures POTTS PUFFY TUMOUR. PRADERWILLI SYNDROME. PREAURICULAR APPENDAGES. PRUNE BELLY.prune belly syndrome. PSEUDOMONAS. PSEUDOMONAS ULCER. PSORIASIS. PUBERTY, PRECOCIOUS. http://www.lib.uct.ac.za/ich/slides/slides.php3?searchfor='P%'

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