Degos Disease An in depth look at degos disease including prognosis and treatment. http://www.thedoctorsdoctor.com/diseases/degos_disease.htm
Extractions: Background This rare disease is important because a skin biopsy may be the first clue to the diagnosis. Patients classically develop multiple skin papules that evolve to have a dimpled appearance with a porcelain white center. This is the clue to the underlying disease which can affect the gastrointestinal tract and central nervous system and may lead to death. The skin biopsy places the pathologist at the center of the diagnostic evaluation. SYNONYMS Malignant Atrophic Papulosis Köhlmeier-Degos' disease INCIDENCE Rare DISEASE ASSOCIATIONS CHARACTERIZATION Familial cases Rare PATHOGENESIS CHARACTERIZATION Unknown-has been considered a vasculitis, mucinosis, or thrombotic disorder No circulating immune complexes, anti-endothelial cell antibodies, or anticardiolipin antibodies identified Endovasculitis Some consider a primary endothelial cell defect with secondary thrombosis leading to infarctive changes LABORATORY/RADIOLOGIC/OTHER TESTS CHARACTERIZATION Impaired fibrinolytic activity Alterations in platelet function GROSS APPEARANCE/CLINICAL VARIANTS CHARACTERIZATION Classic Skin Lesions Crops of papules ranging from 0.5-1 cm which develop an umbilication with a porcelain white center with a telangiectatic ring
Degos Disease Judth Calder's support network for this rare vasculitis.Category Health Conditions and Diseases Rare Disorders Degos Zouboulis. How or why is he involved with degos disease? This is where I'll be postingall my news about degos disease. posted on Sunday, January 20, 2002 http://www.hodgers.com/degos/
Extractions: Tell me again about this Prof. Zouboulis. How or why is he involved with Degos Disease? I can't remember how you came into contact with him and why he would be interested in hosting a conference. Also...do you have any idea yet what this conference purpose would be? And what our (the Dego's Patient) involvement would be? In August last year I got hold of the German "Dermatology" journal - it had only just been published. In it was an article which described the apparently successful treatment of a Degos patient. (Incidentally, it is named after Prof Robert Degos, a Frenchman....).The treatment was Trental - a vaso-dilator. My family doctor put me on it straight away . I rang the Berlin hospital which appeared under the names of the doctors, and asked if I could go and see them (cheeky bugger, aren't I?) They said OK, because they are always fascinated by such a rarity. So I went over with my husband and saw the doctors. They are lovely people and they speak excellent English - I think they've worked in America. They asked to see me again in December, by which time I had been taking the Trental for 4 months. They could see an improvement and asked me a million questions and showed me to a crowd of doctors from the hospital.
Degos Disease - 1 Dept. of Dermatology University of Iowa College of Medicine. Degos' Disease - Malignant Atrophic Papulosis http://tray.dermatology.uiowa.edu/Degos01.htm
Degos Disease - Information For Patients And Doctors degos disease information for patients and doctors. NZ DermNet is an online dermatology resource for patients, GPs and dermatologists conditions Patient Information - degos disease. degos disease. degos disease, also known as malignant atrophic http://www.dermnetnz.org/dna.degos/degos.html
Extractions: Home Skin conditions Degos disease, also known as malignant atrophic papulosis is a rare disorder. It generally occurs in young Caucasian adults. Degos disease affects the lining of the small blood vessels resulting in occlusion (blockage). The blood vessels affected include those supplying the skin, gastrointestinal tract and central nervous system. New lesions What is the cause of Degos disease? The underlying cause of the occlusion of the blood vessels in Degos disease is unknown. Three possible mechanisms are: What are its features? Skin lesions are the characteristic feature of Degos disease. The lesions are usually multiple and occur predominantly on the trunk and arms. They usually start as small red raised spots of 2-5mm in diameter. After a few days they enlarge and develop a central white spot that is depressed in comparison to the red skin around it. They heal leaving depressed porcelain-white scars. Gastrointestinal complications result from lack of blood supply to the lining of the gut and may lead to serious complications like perforation of the bowel. The usual symptoms are sudden onset of abdominal pain or gastrointestinal bleeding (vomiting blood or passing blood with the bowel motion).
Eastern Mediterranean Health Journal, Vol. 6 No. 1, Degos Disease In A 24-year-o degos disease in a 24year-old Jordanian male R.M. Al-Smadi, F. Abu-Jamous and I. Omeish Volume 6, Issue 1, 2000, Page 194-196 Introduction degos disease (malignant atrophic papulosis) is a rare disease that affects skin and the gastrointestinal http://www.emro.who.int/Publications/EMHJ/0601/25.htm
Extractions: Degos disease in a 24-year-old Jordanian male R.M. Al-Smadi, F. Abu-Jamous and I. Omeish Volume 6, Issue 1, 2000, Page 194-196 Introduction Degos disease (malignant atrophic papulosis) is a rare disease that affects skin and the gastrointestinal, ocular and central nervous systems. The disease is characterized by papules that develop porcelain-white centres and telangiectatic borders. The etiology of the disease is unknown; however, the immediate cause may lie in impaired endothelial function or abnormal coagulation (fibrinolytic activity). Viral causes have been implicated. Histopathological findings are wedge-shaped areas of dermal necrosis covered by markedly atrophic malpighian layers and collagen with a smudged appearance. Complications of the disease include peritonitis, intestinal perforation and, less frequently, cerebral infarction. There is no effective treatment; however, antiplatelet therapy may be beneficial for patients in whom platelet aggregation is impaired. Prognosis is poor when systemic involvement is found, but seems to be good in benign forms.
Extractions: Post Message FAQ My short history Steffi Degos world conference Judith mother nature's wholesome art Mahalo Wanting to know more Katrina Dowling-Degos Mike Hofmann response to message caron Degos related digestive system complications Bob Elsasser Loved your site. Maggie hey Nadie mother nature's art Arnie mother nature's art Arnie Touched by degos Deanna Dowling Degos Tim People healed of Rare Incurable Disorders at: dave Consultation in Berlin Judith (Critique of Pure Reason, B628) Chip Chipdinger To: Steff in Germany- Degos Mary Frances Thank you Judith Steffi Ehlers reference for doctor Susan Degos Disease Mary Frances Congratulations!
NORD - Degos Disease Offers synonyms, a general discussion and further resources. http://www.stepstn.com/cgi-win/nord.exe?proc=GetDocument&rectype=0&recnu
Healthy Sexuality - Kohlmeier-Degos Disease - Webmd Welcome to the WebMD Healthy Sexuality Center, learn about symptoms, treatments and more for Kohlmeier-degos disease. http://redirect-west.inktomi.com/click?u=http://ads.247wsr.com/6103-5920539-1-8-
Reticular Melanotic Hypermelanoses Dowlingdegos disease, Arch Dermatol 1978;1141150. VARIANTS, Galli-Galli diseaseAn unrecognized entity or an acantholytic variant of Dowling-degos disease? http://www.thedoctorsdoctor.com/diseases/reticular_melanotic_hypermelanoses.htm
Extractions: Background These rare pigmented diseases are all characterized by a peculiar reticulate pigmentation. They are divided into various disease based upon the distribution and associated conditions. OUTLINE Epidemiology Disease Associations Pathogenesis Gross Appearance and Clinical Variants ... Internet Links Hidradenitis suppurativa, Dowling Degos disease and perianal squamous cell carcinoma. Li M, Hunt MJ, Commens CA. Department of Dermatology, Westmead Hospital, Sydney, New South Wales, Australia. Australas J Dermatol 1997 Nov;38(4):209-11 Abstract quote A patient with hidradenitis suppurativa (HS) is described in association with Dowling Degos disease and perianal squamous cell carcinomas. As the initial treatment for HS failed to give any satisfactory relief he sought no further medical help for the subsequent 40 years. This patient illustrates the management difficulties in HS and the need for regular surveillance to exclude the development of anogenital squamous cell carcinoma. Previous reports of hidradenitis suppurativa in association with Dowling Degos disease are reviewed and the aetiology is discussed.
Degos Disease PATIENT SUPPORT NETWORK AND INFORMATION RESOURCE About Judith I am a 55 year old teacher who was diagnosed with this disease in January 1998. I was referred to Dr Peter Coburn, a Consultant Dermatologist in Chichester, UK who correctly diagnosed http://www.hodgers.com/degos/about_judith.shtml
Extractions: It seems that the cells in the walls of the small and medium-sized arteries and veins multiply and close off blood-supply to the skin in the first stage. In some patients the disease does not progress beyond this stage. In others lesions internally may affect the small intestine and other major organs.
Health Library - Degos Disease degos disease. degos disease is a rare systemic disorder that affects small and mediumsized arteries, causing them to become blocked (occlusive arteriopathy). http://health_info.nmh.org/Library/HealthGuide/IllnessConditions/topic.asp?hwid=
Health Library Deep Vein Leg ThrombosisDeep Leg Vein Thrombosis. Deep Vein Thrombosis-Deep LegVein Thrombosis. degos disease. Dehydration. Dejerine Sottas Disease. Dengue Fever. http://health_info.nmh.org/Library/HealthGuide/IllnessConditions/_SearchResults.
Kohlmeier Degos Disease Expand your medical search to other sites by only one click . For MedicalProfessionals only. Kohlmeier degos disease,, Print this article, http://www.amershamhealth.com/medcyclopaedia/Volume IV 1/KOHLMEIER DEGOS DISEAS
Degos' Disease only one click For Medical Professionals only. Degos' disease,,Print this article, (Robert Degos, born 1904, French dermatologist http://www.amershamhealth.com/medcyclopaedia/Volume IV 1/DEGOS DISEASE.asp
Extractions: *For Medical Professionals only, registration required Degos' disease, (Robert Degos, born 1904, French dermatologist) (also called atrophic papulosis), obliterating angitis of unknown origin characterized by cutaneous papules associated with signs of bowel ischaemia, haemorrhage, perforation and obstruction.
NORD - National Organization For Rare Disorders, Inc. degos disease. To purchase fulltext report ($7.50) Copyright 1994, 1999,2000 Synonyms of degos disease Degos Syndrome; Degos-Kohlmeier Disease; http://www.rarediseases.org/search/rdbdetail_abstract.html?disname=Degos Disease
Degos Disease In A Patient With Acquired Immunodeficiency Click here to return to AIDSLINE main menu degos disease in a patientwith acquired immunodeficiency syndrome. J Am Acad Dermatol. http://www.aegis.com/pubs/aidsline/1998/aug/M9881102.html
Extractions: Requena L; Farina C; Barat A; Department of Dermatology, Fundacion Jimenez Diaz, Universidad; Autonoma, Madrid, Spain. Abstract: Malignant atrophic papulosis is a rare disorder characterized by pathognomonic cutaneous lesions that consist of infarctive thrombosis. Visceral involvement often occurs; the gastrointestinal tract and the central nervous system are most frequently involved. Malignant atrophic papulosis has not been previously described in an AIDS patient. We describe a 58-year-old homosexual man with AIDS who developed typical cutaneous lesions of malignant atrophic papulosis. No visceral involvement has been detected in 2 years. Keywords: *Acquired Immunodeficiency Syndrome/COMPLICATIONS *Skin Diseases, Papulosquamous/COMPLICATIONS *Skin Diseases, Vascular/COMPLICATIONS
Extractions: ARTICLE Haut de page A 34-year-old woman presented with macular hyperpigmentation which had appeared progressively over the previous eight years. Her medical and family history was unremarkable. On examination, grouped, small, brownish macules were found in the axillary, inguinal and submammary folds as well as on the arms and the neck ( Figs. 1 and ). The mucous membranes were not affected. The histopathological findings are seen in Figure 3 Histological examination of a lesion showed elongation, tufting, and deep pigmentation of the rete ridges. PAS stain was negative
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